Primary achalasia

Definition

Definition

Primary achalasia is an esophageal motility disorder characterized by difficulty emptying the esophagus resulting from a lack of peristalsis, associated to degeneration of the local nervous system of the esophageal wall.

Symptoms

Pathophysiology

Primary achalasia is a rare pathology, sometimes included in triple A syndrome:

  • achalasia (in English achalasia).
  • Alacrima.
  • Adrenal insufficiency or adrenal insufficiency following resistance toACTH.